Anaesthesia Recommendations for Patients with Loeys-Dietz Syndrome by İsmail Aytaç in PAPN - Lupine Publishers
Although, arterial tortuosity
is observed mostly in the head and neck vessels, it can occur other
vessels as well. The clinical findings for musculoskelatal system
involvement can be arachnodactyly,
joint laxity, pectus deformities, scoliosis, dolichosternomelia,
talipes equinovarus, comptodactyly, and cervical spine instability.
Cardiovascular findings can be aortic diltation and disection, bicuspid
aortic valve, and congenital heart disease
such as atrial septal defect, patent ductus arteriosis. Central nervous
system anomalies such as Chiari malformation and hydrocephalus can be
observed. However, the life treatining complications that determine the
prognosis are mostly cardiovascular system related findings like aortic
root aneurysms, arterial tortuosity, aneurysyms of other vessels, patent
ductus arteriosis, and atrial septal defect - Lupine Publishers.
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